Anemia de células falciformes

Sickle cell anemia

Contenido principal del artículo

Walter Chaves
Dolly Amador
Jorge Sánchez

Resumen

Presentamos dos mujeres que consultaron a urgencias por dolor abdominal agudo, iniciado pocas horas después de su llegada a Bogotá DC, asociado con síndrome anémico y hallazgos paraclínicos sugestivos de anemia de células falciformes, que se confirmó con electroforesis de proteínas en la consulta externa. La drepanocitosis, conocida como anemia de células falciformes, es una hemoglobinopatía estructural de causa genética que ocasiona clínica vasoclusiva con isquemia tisular secundaria generadora de crisis de dolor, que se exacerba entre otras razones por cambios de temperatura y de la presión del oxígeno atmosférico. Es importante causa de dolor agudo en pacientes de raza negra que asisten a urgencias al provenir con frecuencia de lugares cálidos.

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