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Arrhythmogenic right ventricular dysplasia

Displasia arritmogénica del ventrículo derecho




Section
Case Reports

How to Cite
Chaves, J. J., Niño, C., Bryon, A., Medina, H., Calle, F., Fernando Polo, J., & Parra Medina, R. (2019). Arrhythmogenic right ventricular dysplasia. Journal of Medicine and Surgery Repertoire, 28(1). https://doi.org/10.31260/RepertMedCir.v28.n1.2019.878

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Juan José Chaves
    Caterin Niño
      Adriana Bryon
        Hernán Medina
          Francisco Calle
            José Fernando Polo
              Rafael Parra Medina

                Arrhythmogenic right ventricular dysplasia (ARVD) is a cardiomyopathy inherited in an autosomal dominant pattern characterized by replacement of myocytes with fibrofatty tissue. ARVD is the second cause of sudden death in young adults and accounts for a great proportion of deaths in athletes. Clinical presentation is variable, it may occur during rest or after physical activity involving unspecific symptoms such as palpitations, syncope and chest pain. We here report three autopsy cases, referred from various healthcare institutions, in which sudden death was the first manifestation.


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