Giant pheochromocytoma

Feocromocitoma gigante

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Angélica Maria Fonseca
William Rojas

Abstract

Pheochromocytoma is a neuroendocrine neoplasia of chromaffin cells that biosynthesizes, stores, metabolizes and secretes high concentrations of catecholamines and their metabolites. The incidence is of two to eight cases per million and is frequent in the fourth and fifth decades of life. Case presentation: a 19-year-old woman with high blood pressure in medical checkups due to a history of asthma since childhood, which is studied with biochemical analysis and abdominal CT. Surgery was taken due to the suspicion of an adrenal tumor and the neoplasm is characterized in the pathology department. Conclusions: the diagnosis of pheochromocytoma and sympathetic paragangliomas that synthesize and secrete catecholamines (adrenaline, noradrenaline and dopamine) is based on the physical examination and the analytical study; The main symptom is hypertension. The treatment is surgical with complete healing in more than 90%. Abbreviations: FC, pheochromocytoma (s); PG, paraganglioma (s).

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References

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