Medical management of patients with hemophilia A, B and Von Willebrand disease who underwent surgery a sixteen year experience at Hospital de San José, Bogotá

Objetivo: describir el manejo médico de tipo hemostático durante el pre, trans y posoperatorio de pacientes con hemofilia y enfermedad de von Willebrand. Materiales y métodos: serie de casos de pacientes diagnosticados con hemofilia A, B, enfermedad de vo

Objective: to describe haemostatic management of patients with hemophilia and von Willebrand disease before, during and after surgery. Materials and Methods: case series of patients diagnosed with hemophilia A, B, von Willebrand disease and factor VII deficiency, from January 1993 to June 2009 at Hospital de San José, Bogotá DC. Results: 35 scheduled surgeries of various specialties in 28 patients (4 females, 24 males). For those with hemophilia A and B the objective in terms of level of haemostasis in orthopedic procedures was: on day one 100%, from day two to five: 74% and day 6 and so on: 60%; in dental procedures, on day one the factor was corrected an average of 85% and from day two to five: 65%. Patients with Von Willebrand disease were managed with a 50 IU/k dose every 8 to 24 hours. There were 3 cases of infection and no deaths occurred. Conclusions: Hospital de San José has gained a vast experience in conducting scheduled surgical procedures in patients with hemophilia A, B and von Willebrand disease. These patients have been managed successfully during these 16 years with a Iow complication rate.

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