Fetal double aortic arch

Doble arco aórtico fetal

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Eduardo Reyna Villasmil

Abstract

Introduction: double aortic arch represents a congenital anomaly in which the right embryonic arch does not involute, resulting in the continuity of the left and right aortic arch, encircling the trachea and esophagus. Case presentation: we present the case of a 21-year-old nulliparous gravida that was referred to prenatal care due to the suspicion of fetal cardiac alterations. Prenatal ultrasound scanning revealed four brachiocephalic vessels emerging from the right superior vena cava suggesting a symmetrical double aortic arch. Both arches encircled the trachea and the esophagus to form a vascular ring around these structures, joining to form a left-sided normal caliber descending aorta. Postnatal echocardiography demonstrated a patent right dominant aortic arch and an atretic left aortic arch. Discussion: the aortic arch courses right to the trachea and bifurcates to form a right and left arch. Posterior to the trachea, the arches merge into the descending aorta, that runs in the midline and lies in front of the vertebral column. Conclusion: double aortic arch is a rare anomaly with potentially negative consequences. Prenatal diagnosis allows early surgical repair and adequate follow-up to prevent the development of airway damage.


 

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